A case of arrhythmogenic right ventricular cardiomyopathy with biventricular involvement

Submitted: November 16, 2018
Accepted: February 25, 2019
Published: March 27, 2019
Abstract Views: 1001
PDF: 708
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Authors

We reported a case of a young adult male aged 18 years admitted in our institution for syncope during a basketball match. No previous symptoms were reported. Electrocardiogram (ECG) showed T-wave inversion in the anterior leads and an incomplete right bundle branch block. Surprisingly, a complete echocardiographic evaluation demonstrated the presence of severe right ventricular enlargement with significant wall motion abnormalities, apical aneurysm and reduced systolic function. Cardiac Magnetic Resonance was pathognomonic for a fibro-fatty replacement of both ventricles. We decided for a subcutaneous defibrillator implantation and, after inducing a ventricular fibrillation to test the device status, epsilon wave appeared on the ECG. This clinical scenario depicted an advanced arrhythmogenic right ventricular cardiomyopathy at its first clinical manifestation.

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Brandimarte, Filippo, Alessandro Battagliese, Silvana Petronilla Pirillo, Maria Teresa Mallus, Rosa Maria Manfredi, and Giovanni Carreras. 2019. “A Case of Arrhythmogenic Right Ventricular Cardiomyopathy With Biventricular Involvement”. Monaldi Archives for Chest Disease 89 (1). https://doi.org/10.4081/monaldi.2019.1009.