Erasmus syndrome: The association of systemic sclerosis and silicosis

Submitted: February 3, 2022
Accepted: April 7, 2022
Published: April 12, 2022
Abstract Views: 1173
PDF: 332
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Erasmus syndrome is the association of the exposure to silica and the subsequent development of systemic sclerosis, a rare occurrence, with scarce data in medical literature, which can be attributed to little knowledge of the syndrome and underdiagnosis. It is important to recognize this association as it has a worse respiratory prognosis than the idiopathic form of systemic sclerosis and since autoimmune diseases are rarer in men, it is easy to do exposure research when they occur. We describe the case of a 59-year-old man, a bricklayer by craft since the age of 15, who presented with respiratory symptoms and skin alterations and in whom this syndrome was diagnosed during his recent admission.



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How to Cite

Osejo-Betancourt, Miguel, and Pedro Chaparro-Mutiz. 2022. “Erasmus Syndrome: The Association of Systemic Sclerosis and Silicosis”. Monaldi Archives for Chest Disease 93 (1).