Hamman-Rich syndrome: a forgotten entity

Submitted: November 25, 2016
Accepted: April 10, 2017
Published: May 18, 2017
Abstract Views: 1620
PDF: 810
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The following report outlines the case of a 76-year-old gentleman who presented to the hospital with acute interstitial pneumonitis, a rare and rapidly progressive type of idiopathic interstitial pneumonia. The patient initially presented with a three-week history of progressive shortness of breath and cough which was diagnosed as community acquired pneumonia. Treatment with oral antibiotics was unsuccessful resulting in re-presentation the following week with type one respiratory failure. Investigations revealed widespread inflammatory changes consistent with an acute inflammatory process. Intravenous steroids, antibiotics and antiviral medications were initiated before an urgent transfer to the intensive care unit was required for intubation. An open lung biopsy, in conjunction with the clinical picture, confirmed the diagnosis of acute interstitial pneumonitis. The significance of this report is to highlight the rapid and destructive clinical course of a rare type of pneumonitis, which initially presented as a routine and innocuous diagnosis in our patient.



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How to Cite

Newmarch, William, Angelica Puopolo, Madina Weiler, and Brian Casserly. 2017. “Hamman-Rich Syndrome: A Forgotten Entity”. Monaldi Archives for Chest Disease 87 (1). https://doi.org/10.4081/monaldi.2017.799.