Hammering home the sickle: an instructive case of endobronchial anaplastic large cell lymphoma



  • Mohammad Abu-Hishmeh | memaad@hotmail.com Division of Pulmonary, Critical Care, and Sleep Medicine, Baystate Medical Center, Springfield, MA, United States. https://orcid.org/0000-0002-6338-0325
  • Laura Miranda Division of Pulmonary, Critical Care, and Sleep Medicine, Westchester Medical Center, Valhalla, NY, United States. https://orcid.org/0000-0003-2973-5695
  • Fouzia Shakil Department of Pathology, Westchester Medical Center, Valhalla, NY, United States.
  • Tauseef Ahmed Division of Medical Oncology, Westchester Medical Center, Valhalla, NY, United States.
  • Oleg Epelbaum Division of Pulmonary, Critical Care, and Sleep Medicine, Westchester Medical Center, Valhalla, NY, United States.


It is extremely unusual for primary pulmonary lymphoma, an uncommon occurrence in any form, to be of T-cell origin and to manifest as an endobronchial lesion. Each of these characteristics is rare individually, so cases that combine them are exceptional. We report a patient in whom primary pulmonary anaplastic large cell lymphoma, a T-cell neoplasm, presented with obstruction of the left upper lobe bronchus, resulting in left upper lobe atelectasis and creating the radiographic luftsichel sign. We briefly discuss anaplastic large cell lymphoma as a whole, place our case in the context of previously published literature on endobronchial anaplastic large cell lymphoma, and review the genesis of the luftsichel sign.     



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Pneumology - Case Reports
primary pulmonary lymphoma, anaplastic large cell lymphoma, luftsichel sign
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How to Cite
Abu-Hishmeh, Mohammad, Laura Miranda, Fouzia Shakil, Tauseef Ahmed, and Oleg Epelbaum. 2021. “Hammering Home the Sickle: An Instructive Case of Endobronchial Anaplastic Large Cell Lymphoma”. Monaldi Archives for Chest Disease, April. https://doi.org/10.4081/monaldi.2021.1601.